Journal Article10.3171/2010.12.PEDS10379
Institutional experience with 500 cases of surgically treated pediatric Chiari malformation Type I.
R. Shane Tubbs,Joshua M. Beckman,Robert P. Naftel,Joshua J. Chern,John C. Wellons,Curtis J. Rozzelle,Jeffrey P. Blount,W. Jerry Oakes +7 more
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TL;DR: This is believed to be the largest reported series of surgically treated pediatric Chiari malformation Type I patients and the authors hope that their experience will be of use to others who treat this surgical entity.
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Abstract: Object The diagnosis and treatment of Chiari malformation Type I (CM-I) has evolved over the last few decades. The authors present their surgical experience of over 2 decades of treating children with this form of hindbrain herniation. Methods The authors conducted a retrospective review of their institutional experience with the surgical treatment of the pediatric CM-I from 1989 to 2010. Results The 2 most common presentations were headache/neck pain (40%) and scoliosis (18%). Common associated diagnoses included neurofibromatosis Type 1 (5%) and idiopathic growth hormone deficiency (4.2%). Spine anomalies included scoliosis (18%), retroversion of the odontoid process (24%), Klippel-Feil anomaly (3%), and atlantooccipital fusion (8%). Approximately 3% of patients had a known family member with CM-I. Hydrocephalus was present in 48 patients (9.6%). Syringomyelia was present in 285 patients (57%), and at operation, 12% of patients with syringomyelia were found to have an arachnoid veil occluding the fourth...
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Pediatric and adult Chiari malformation Type I surgical series 1965–2013: a review of demographics, operative treatment, and outcomes
TL;DR: Before undergoing surgical treatment for CM-I, symptomatic patients and their families should be given clear information about the success of treatment and potential complications, and surgeons may benefit from comparing published data with their own.
231
Neurological and spinal manifestations of the Ehlers–Danlos syndromes
Fraser Henderson,Claudiu Austin,Edward C. Benzel,Paolo A. Bolognese,Richard G. Ellenbogen,Clair A. Francomano,Candace Ireton,Petra M. Klinge,Myles Koby,Donlin M. Long,Sunil J. Patel,Eric L. Singman,Nicol C. Voermans +12 more
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Surgical treatment of Chiari I malformation--analysis of intraoperative findings, complications, and outcome for 371 foramen magnum decompressions.
TL;DR: Arachnoid pathology in Chiari I malformation has an impact on clinical symptoms and postoperative results and decompressions performed by surgeons experienced with this pathology offer a favorable long-term prognosis.
207
The Chiari I malformation.
TL;DR: A review of Chiari I malformation and its associated entities can be found in this paper, where the authors discuss the evolution in understanding of the Chiari malformation, distinguish between symptomatic CIM and asymptomatic tonsillar ectopia, and discuss techniques for surgical intervention, expected outcomes, and complications after surgery.
References
Basichondrocranium anomalies in adult Chiari type I malformation: a morphometric study.
TL;DR: It is proved that under-development of the basichondrocranium with a small size of the posterior fossa is an outstanding feature in adult Chiari type I malformation, and the hypothesis that tonsillar ectopia is secondary to the disproportion between the posterior Fossa and the cerebellum, which is forced to grow into the cervical spinal canal is supported.
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Surgical treatment of syringomyelia based on magnetic resonance imaging criteria.
Thomas H. Milhorat,Walter D. Johnson,John I. Miller,Richard M. Bergland,Joanna R. Hollenberg-Sher +4 more
TL;DR: A retrospective study of 65 patients with cavitary lesions of the spinal cord in whom the results of magnetic resonance imaging were used to develop specific treatment strategies for syringomyelia reports a retrospective study.
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Chiari type I malformation in children
TL;DR: Magnetic resonance imaging was essential to the diagnosis; the presence of tonsillar herniation was confirmed at surgery and the results of suboccipital decompression were favorable in this series.
139
Chiari I Malformation: A Review of 43 Patients
Virinder Nohria,Jerry Oakes +1 more
TL;DR: It was able to show the patients who did not have hydrosyringomyelia were unlikely to develop scoliosis and there was positive correlation between improvement in hydrosyringsomyelia and the improvement in signs and symptoms.
120
Scoliosis associated with syringomyelia presenting in children.
Toyohiko Isu,Yoshimi Chono,Yoshinobu Iwasaki,Izumi Koyanagi,Minoru Akino,Hiroshi Abe,Kuniyoshi Abumi,Klyoshi Kaneda +7 more
TL;DR: The authors think that the scoliosis develops in children as a result of damage done to the anterior horn, which innervates the muscles of the trunk, by an asymmetrically expanded syrinx.
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