T. E. Stacey
University of North Carolina at Chapel Hill
12 Papers
114 Citations
T. E. Stacey is an academic researcher from University of North Carolina at Chapel Hill. The author has contributed to research in topics: Carnitine & Diet therapy. The author has an hindex of 8, co-authored 12 publications.
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Papers
Metabolic response to carnitine in methylmalonic aciduria. An effective strategy for elimination of propionyl groups.
TL;DR: Giving carnitine to a patient with methylmalonic aciduria produced an increase in hippurate excretion, an index of intramitochondrial adenosine triphosphate (ATP) and CoA availability, a large increase in short chain urinary acylcarnitines, and a reduction in excretion of methylmalonate and methylcitrate.
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The response to L-carnitine and glycine therapy in isovaleric acidaemia.
TL;DR: L-carnitine supplementation is of value in the treatment of isovaleric acidaemia and that, in the present case, l-c Carnitine together with a moderate dietary restriction has proved to be the optimum form of therapy.
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L-Carnitine insufficiency in disorders of organic acid metabolism: response to L-carnitine by patients with methylmalonic aciduria and 3-hydroxy-3-methylglutaric aciduria.
Ronald A. Chalmers,T. E. Stacey,B. M. Tracey,C. de Sousa,Charles R. Roe,David S. Millington,Charles L. Hoppel +6 more
TL;DR: The concept of a general approach to the treatment of patients with disorders of organic acid metabolism, that of L-carnitine therapy, has been developed from the observations.
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Dizygotic twins with 3-hydroxy-3-methylglutaric aciduria; unusual presentation, family studies and dietary management
T. E. Stacey,C. de Sousa,B. M. Tracey,Andrew Whitelaw,J. Mistry,P. Timbrell,Ronald A. Chalmers +6 more
TL;DR: Examination of the urine for organic acids should be considered in infants with unexplained hypotonia and macrocephaly, especially if accompanied by abnormal biochemical indices.
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Acylcarnitines in urine in medium-chain acyl-CoA dehydrogenase deficiency measured by quantitative high-pressure liquid chromatography
TL;DR: A review of current literature on the regulation of Liver Metabolism and Lipids I1 by Bone, A. J., Sherratt, H. S. & Turnbull, D. M.
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